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Etiology, Epidemiology, Patho Physiology Diagnosis, Treatment and Differential Diagnosis of Hemochromatosis

Guruprasad M., Muralinath E., Pooja Devi, Prasanta Chbukdhara, Sanjib Borah, Kalyan C., Archana Jain

Abstract


A patient's history of iron excess linked to chronic anemia, alcoholic liver disease, multiple transfusions, inefficient erythropoiesis with marrow hyperplasia, and porphyria cutanea tarda should all be taken into consideration during the evaluation process. Other bacterial illnesses that could affect the patients include meningitis brought on by Listeria monocytogenes, liver abscesses caused by Yersinia enterocolitica, sepsis from Vibrio vulnificus, and sepsis from pseudotuberculosis.  Keep in mind that individuals with hemochromatosis who also have cirrhotic livers have a higher chance of developing hepatoma. Differentiating between hemochromatosis arthropathy and rheumatoid arthritis is important for a number of reasons. For example, corticosteroids are not necessary for patients with hereditary hemochromatosis. Moreover, delayed phlebotomy treatment and a failure to seek familial genetic counseling could result from inaccurate rheumatoid arthritis diagnosis.


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