A Review of Mayer Rokitansky Kuster Hauser Syndrome

Abstract

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital disorder characterized by the absence or underdevelopment of the vagina and uterus, affecting approximately 1 in 4,500 to 1 in 5,000 female infants. Management involves a multidisciplinary approach, including medical, surgical, and psychological interventions. Vaginal dilation therapy, vaginal reconstruction surgery, and hormone replacement therapy may be necessary. MRKH syndrome is a complex and multifaceted condition requiring comprehensive and individualized management. Early diagnosis and intervention can significantly improve quality of life and fertility outcomes for affected individuals.